Central auditory processing disorder associated with moyamoya disease

Moyamoya disease is a rare, progressive, occlusive cerebrovascular condition that has previously been noted to be associated with cortical deafness. Other forms of auditory deficit, such as auditory processing disorder, have rarely been considered in the assessment of patients with moyamoya disease. A case of central auditory processing disorder is presented in a 26-year-old female of Chinese ethnicity with moyamoya disease. The patient had bilateral, near-normal hearing thresholds and normal immittance audiometry results. However, she displayed poor speech perception in noise and her results for other auditory processing tasks were markedly abnormal. These findings suggest that patients with moyamoya disease may benefit from a full auditory assessment that includes tests of auditory processing skills.